- A Case of Desensitization for Hemophilia B Inhibitor Patient with Anaphylaxis to FIX Concentrates
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Park Y, Yoo KY
- KMID: 2252186
- Korean J Hematol.
- 2008 Sep;43(3):179-183.
- doi: 10.5045/kjh.2008.43.3.179
Among the patients with hemophilia, 10~15% have hemophilia B, and 1~3% of the hemophilia B patients develop inhibitor to factor IX clotting activity. Allergic reactions to concentrates containing factor IX... -
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- A Case of Hemophilia B Diagnosed after Rhinosinus Surgery in 37 Year-Old Patient
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Kim HD, Choi IS
- KMID: 2436473
- Korean J Otorhinolaryngol-Head Neck Surg.
- 2018 Jun;61(6):308-311.
- doi: 10.3342/kjorl-hns.2016.17489
Hemophilia is an X-linked recessive disorder, which is classified into hemophilia A, defined by factor VIII deficiency and hemophilia B, defined by factor IX deficiency. The usual clinical presentation is... -
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- Hemophilia
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Yoo KY
- KMID: 1607306
- Korean J Pediatr.
- 2006 Aug;49(8):821-829.
- doi: 10.3345/kjp.2006.49.8.821
Hemophilia is the most common coagulation disorder. It has a long history. Hemophilia A is caused by FVIII gene mutation, and hemophilia B by FIX gene mutation. Those genes are... -
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- Bone Density Status in Bleeding Disorders: Where Are We and What Needs to Be Done?
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Mansouritorghabeh H, Rezaieyazdi Z
- KMID: 2397552
- J Bone Metab.
- 2017 Nov;24(4):201-206.
- doi: 10.11005/jbm.2017.24.4.201
Bleeding disorders, including hemophilia, can be seen in every ethnic population in the world. Among various bleeding disorders, reduced bone density has been addressed in hemophilia A. In recent years,... -
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- Recent Advance of Pharmacotherapy in Hemophilia
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Park YS
- KMID: 2188133
- J Korean Med Assoc.
- 2009 Dec;52(12):1201-1206.
- doi: 10.5124/jkma.2009.52.12.1201
Hemophilia A (factor VIII deficiency) and Hemophilia B (factor IX deficiency) are the most common and serious congenital coagulation disorders. Accurate diagnosis is important and essential for effective management. A... -
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- The first case report of a patient with coexisting hemophilia B and Down syndrome
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Rastogi P, Kumar N, Ahluwalia , Das R, Panigrahi
- KMID: 2375212
- Blood Res.
- 2017 Mar;52(1):75-76.
- doi: 10.5045/br.2017.52.1.75
No abstract available. -
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- Usefulness of HhaI and MseI DNA Polymorphism of Factor IX Gene in the Molecular Genetic Diagnosis of Hemophilia B in Korean Population
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Lee JH, Choi YM, Choe J, Hwang DY, Lee JY
- KMID: 2261608
- Korean J Obstet Gynecol.
- 1999 Dec;42(12):2761-2767.
OBJECTIVES: Hemophilia B has been known to result from more than 500 kinds of mutations. And it is difficult to find out a mutation specific for each family. Therefore, linkage... -
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- Emergency Department Visits in Hemophilia Patients
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Kim M, Ryu M, Lee JE, Park J, Lee S
- KMID: 1807600
- Clin Pediatr Hematol Oncol.
- 2013 Oct;20(2):86-94.
BACKGROUND: Hemophilia A and hemophilia B are characterized by prolongation of bleeding and hemorrhages in the joints and soft tissues. There is no ultimate treatment, if patients did not properly... -
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- A Case of Repeated Cesarean Section on the Patient who has a Moderate Hemophilia B
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Lee DN, Oh YJ, Kyung YS, Yoon SW, Choi JS, Kim KH, Lee KW, Kim SD, Han JS
- KMID: 2272211
- Korean J Obstet Gynecol.
- 2003 Nov;46(11):2317-2322.
Hemophilia is a hemorrhagic disease caused by the defect or abnormal activities of the coagulation factor. The proper dosage and interval of factor replacement therapy are not defined. So the... -
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- A Case of Anaphylactic Response to Factor lX Replacement Therapy in Hemophilia B Patient
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Shin SA, Kim YD, Lee H
- KMID: 2252405
- Korean J Hematol.
- 2003 Aug;38(3):188-190.
We report a first korean case of anaphylactic response to factor lX replacement therapy in 22-month-old male hemophilia B patient. He was admitted to our hospital via emergency room due... -
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- Moderate Hemophilia B Diagnosed by Massive Gastrointestinal Hemorrhage on the First Day of Life: A Case Report and Literature Review
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Park SH, Choe BH
- KMID: 2360465
- Neonatal Med.
- 2016 Nov;23(4):238-241.
- doi: 10.5385/nm.2016.23.4.238
Gastrointestinal hemorrhage in neonates is commonly associated with necrotizing enterocolitis, cow's milk protein allergy, and gastrointestinal malformation. Gastrointestinal bleeding on the first day of life, presenting as the first manifestation... -
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- A Case of Heel Reconstruction with a Reverse Sural Artery Flap in a Hemophilia B Patient
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Lee BK, Shim JS
- KMID: 1921079
- Arch Plast Surg.
- 2012 Mar;39(2):150-153.
- doi: 10.5999/aps.2012.39.2.150
Hemophilia B is a rare blood coagulation disorder. Complications such as bleeding and hematoma can cause necrosis of flaps, wound disruption, and the disturbance of wound healing. In particular, guidelines... -
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- Septic Arthritis and Infective Endocarditis in an Adolescent Hemophilia B Patient with an Inhibitor and a Central Venous Access Device
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Kim J, Park YS
- KMID: 2435426
- Clin Pediatr Hematol Oncol.
- 2018 Apr;25(1):61-65.
- doi: 10.15264/cpho.2018.25.1.61
Central venous access devices (CVAD) provide hemophilic patients, particularly children, with prolonged reliable venous access to promote routine factor replacement therapy. However, one of the significant complications of CVAD use... -
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- Global hemostatic assay of different target procoagulant activities of factor VIII and factor IX
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Yoo KY, Jung SY, Hwang SH, Lee SM, Park JH, Nam HJ
- KMID: 2414363
- Blood Res.
- 2018 Mar;53(1):41-48.
- doi: 10.5045/br.2018.53.1.41
BACKGROUND: Korean National Health Insurance reimburses factor VIII (FVIII) and factor IX (FIX) clotting factor concentrate (CFC) infusions to discrepant activity levels, allowing elevation of FVIII activity to 60 IU/dL... -
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- A Case Peport of Hemphilia B (Christmas Disease)
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Lim BS, Lee JK, Shin DC
- KMID: 1660921
- J Korean Pediatr Soc.
- 1977 Jun;20(6):467-471.
We have reported on a case of hemophilia B (Christmas disease) of 6 month old Korean who was have admitted to our hospital in duration of 7 days on Aug.... -
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- Maintenance Therapy with Activated Prothrombin Complex Concentrate (aPCC) for Hemophilia Patients with High Levels of Responding Inhibitors
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Yoo KY, Choi YM, Park YS
- KMID: 2252098
- Korean J Hematol.
- 2009 Dec;44(4):205-211.
- doi: 10.5045/kjh.2009.44.4.205
BACKGROUND: Eleven percent of severe hemophilia A patients and 5% of severe hemophilia B patients may develop inhibitors. We have conducted aPCC-based maintenance therapy for hemophilia patients with high levels... -
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- Human parvovirus B19 and parvovirus 4 among Iranian patients with hemophilia
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Javanmard , Ziaee M, Ghaffari H, Namaei MH, Tavakoli A, Mollaei H, Moghoofei , Mortazavi , Monavari S
- KMID: 2405069
- Blood Res.
- 2017 Dec;52(4):311-315.
- doi: 10.5045/br.2017.52.4.311
BACKGROUND: Human parvovirus B19 (B19V) is one of the smallest DNA viruses and shows great resistance to most disinfectants. Therefore, it is one of the common contaminant pathogens present in... -
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- TKA in Hemophilic Arthropathy of the Knee
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Bae DK, Yim CM, Jeon MH, Cha JR
- KMID: 2189442
- J Korean Orthop Assoc.
- 1999 Jun;34(3):489-494.
PURPOSE: To analyze functional gains after TKA in patients with hemophilic arthropathy. MATERIALS AND METHODS: From January 1989 to December 1996, 16 total knee replacements were performed in 11 patients... -
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- Perioperative Management of Patients with Hemophilia during Spinal Surgery
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Kobayashi , Imagama S, Ando K, Ito K, Tsushima M, Morozumi M, Tanaka S, Machino M, Ota K, Nishida Y, Ishiguro N
- KMID: 2430658
- Asian Spine J.
- 2018 Jun;12(3):442-445.
- doi: 10.4184/asj.2018.12.3.442
STUDY DESIGN: Single-center retrospective study. PURPOSE: To optimize the perioperative management of patients with hemophilia who are undergoing spinal surgery. OVERVIEW OF LITERATURE: Hemophilia is a rare disease in which there is... -
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- Prevalence, Incidence, and Factor Concentrate Usage Trends of Hemophiliacs in Taiwan
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Tu TC, Liou WS, Chou TY, Lin TK, Lee CF, Chen JD, Cham TM, Chung MI
- KMID: 1776920
- Yonsei Med J.
- 2013 Jan;54(1):71-80.
- doi: 10.3349/ymj.2013.54.1.71
PURPOSE: Hemophilia A and B (HA, HB) are the most common X-linked inherited bleeding disorders. The introduction of factor concentrates has allowed for control of the lifelong chronic disease. However,... -
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